Paper

Atresia of Proximal Coronary Arteries in Pulmonary Atresia with Intact Ventricular Septum – Fetal and Neonatal Findings
Taisto Sarkola^a, Talvikki Boldt^a, Juha-Matti Happonen^a, Riitta Karikoski^b, Marianne Eronen<sup>c

a</sup>Division of Pediatric Cardiology, Department of Pediatrics and
^bHUSLAB, HUCH Hospital for Children and Adolescents, and
^cSocial Insurance Institution of Finland, Helsinki, Finland

Address of Corresponding Author

Fetal Diagn Ther 2008;24:413-415 (DOI: 10.1159/000168675)

  Key Words

• Pulmonary atresia with intact ventricular septum
• Coronary atresia
• Congenital heart disease
• Fetal echocardiography

  Abstract

Pulmonary atresia with intact ventricular septum (PA+IVS) is a rare congenital cardiac malformation which is associated with ventriculocoronary arterial communications from the right ventricle. We present a case of PA+IVS with a bilateral atresia of the coronary ostia, and thus, a completely right ventricular-dependent coronary circulation followed up by fetal echocardiography. Eventually the infant died of myocardial infarction at 2 days of age.

Copyright © 2008 S. Karger AG, Basel

  Author Contacts

Taisto Sarkola, MD, PhD
Division of Pediatric Cardiology, Department of Pediatrics
HUCH Hospital for Children and Adolescents
POB 281, FI–00029 HUS, Helsinki (Finland)
E-Mail taisto.sarkola@hus.fi

  Article Information

Received: September 6, 2007
Accepted after revision: November 6, 2007
Published online: November 6, 2008
Number of Print Pages : 3
Number of Figures : 3, Number of Tables : 1, Number of References : 18