Address of Corresponding Author

Pancreatology 2005;5:289-294 (DOI: 10.1159/000085285)

  Key Words

• Solid-papillary cystic tumor
• Surgery
• Liver metastases

  Abstract

The solid-pseudopapillary tumor (SPT) is a very rare pancreatic neoplasm that predominantly affects young females. About 450 cases have been described in the world literature and approximately 20% of the reported patients were children. The occurrence of SPT with distant metastases in children is extremely rare with only two previously reported cases. We now report a 16-year-old Asian girl with a large SPT and synchronous multiple liver metastases who was successfully treated in a 2-step strategy, including initial pylorus-preserving partial duodenopancreatectomy, right hemicolectomy, resection and allografting of the portal vein and secondary resection of 12 liver metastases. The patient is disease free after a follow-up of 18 months after resection of the primary tumor, suggesting that an aggressive surgical treatment might also be justified for metastasized SPT.

Copyright © 2005 S. Karger AG, Basel and IAP

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  Author Contacts

D.K. Bartsch
Department of Surgery Philipps University Marburg
DE-35033 Marburg (Germany)
Tel. +49 6421 286 64 43, Fax +49 6421 286 89 95
E-Mail bartsch@mailer.uni-marburg.de

  Article Information

Published online: April 22, 2005
Number of Print Pages : 6
Number of Figures : 3, Number of Tables : 0, Number of References : 25

  Publication Details

Pancreatology

Vol. 5, No. 2-3, Year 2005 (Cover Date: 2005)

Journal Editor: Urrutia, R. (Rochester, Minn.)
ISSN: 1424-3903 (print), 1424-3911 (Online)

For additional information: http://www.karger.com/pan

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